This mutated SOD1 protein reacts with some anomalous substrates such as hydrogen peroxide using it as a substrate and produces the most reactive hydroxyl radical which can severely damage important biomolecules [146]

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Wang R, Qiu M, Zhang L, Sui M, Xiao L, Yu Q, et al
Endogenous OSCs include methionine, cysteine, universal methyl donor s-adenosyl-l-methionine (SAM), homocysteine, cystathionine, cysteine, glutathione (GSH), coenzyme A (CoA), hypotaurine, taurine, and others [4]
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